magistrsko delo
    	
    Abstract
 
Matrin 3 (MATR3) je DNA/RNA-vezavni protein jedrnega matriksa, ki je vključen v 
različne celične procese. Sodeluje pri zgodnjem odzivu na poškodbe DNA, prepisovanju, 
stabilizaciji mRNA, alternativnem izrezovanju intronov in jedrnem izvozu mRNA. 
Mutacija S85C v genu MATR3 je povezana z razvojem počasi napredujoče oblike 
amiotrofične lateralne skleroze (ALS), vendar vloga MATR3 v patogenezi te bolezni ni 
poznana. Slabo opisane in nepoznane so tudi proteinske interakcije MATR3 in njegovih 
mutantov. Prav te pa bi bile lahko odgovorne za razvoj ALS. V sklopu magistrskega dela 
smo želeli z metodo BioID, ki temelji na označevanju bližnjih proteinov z biotinom,
identificirati proteine, ki v pogojih in vivo interagirajo s človeškim MATR3 in njegovo
mutirano obliko MATR3S85C. V ta namen smo pripravili inducibilne ekspresijske celične 
linije HEK 293, ki stabilno izražajo fuzijski protein MATR3 oz. MATR3S85C z biotin 
ligazo BioID2, ali BioID2 brez fuzijskega partnerja. Ugotovili smo, da imata fuzijska
proteina MATR3 in MATR3S85C z BioID2 enako celično lokalizacijo kot endogeni 
MATR3 in da je ligaza BioID2 v teh fuzijah encimsko aktivna. Po preučitvi aktivnosti
BioID2 in celične lokalizacije izraženih proteinov smo nadaljevali s testom »pull down«, 
s katerim smo iz celičnih lizatov uspešno izolirali biotinilirane interakcijske partnerje 
obeh oblik MATR3. Z barvanjem s srebrom in imunodetekcijo biotiniliranih proteinov
po prenosu western smo namreč zaznali proteine, ki so značilni za vzorce z MATR3 in 
MATR3S85C, ne pa tudi za vzorce z BioID2 brez fuzijskega partnerja. Te interakcijske
partnerje bomo identificirali s tehniko tekočinske kromatografije, sklopljene z masno 
spektrometrijo. Rezultati bodo pripomogli k razumevanju interaktoma MATR3 in 
MATR3S85C. V eluatih z MATR3 in MATR3S85C smo sicer že zaznali dva znana 
interakcijska partnerja MATR3, proteina TDP-43 in NONO. Na koncu smo preverili še 
vpliv MATR3S85C na nastanek stresnih granul in na podlagi rezultatov zaključili, da ta 
oblika MATR3 prepreči njihovo tvorbo.
    Keywords
 
amiotrofična lateralna skleroza;ALS;proteini;matrin 3;MATR3;interakcijski partnerji;biotinska identifikacija;BioID;magistrska dela;
    Data
 
    
        
            | Language: |  
            Slovenian | 
        
        
        
            | Year of publishing: |  
            2021 | 
        
            
        
        
            | Typology: |  
            2.09 - Master's Thesis |         
        
            
        
            | Organization: |  
            UL FKKT - Faculty of Chemistry and Chemical Technology |         
        
        
            | Publisher: | 
            [J. Nimac] | 
        
   
        
            | UDC: |  
            577.112:616.8-009.5(043.2) |         
        
   
        
        
            | COBISS: |  
            
                
                    89932291
                     
                
             | 
        
        
        
  
        
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    Other data
 
    
        
            | Secondary language: |  
            English | 
        
        
        
            | Secondary title: |  
            Protein interactions of human matrin 3 | 
        
        
        
        
            | Secondary abstract: |  
            Matrin 3 (MATR3) is a DNA/RNA-binding nuclear matrix protein involved in several 
cellular processes. These include early stages of DNA damage response, transcription, 
mRNA stability, alternative splicing and mRNA export. The mutation S85C in 
the MATR3 gene is associated with the development of a slowly progressive form of 
amyotrophic lateral sclerosis (ALS). However, the role of MATR3 in the pathogenesis of 
this disease is unknown. Additionally, little is known about the protein-protein 
interactions of MATR3 and its mutants, even though these interactions could be 
responsible for ALS development. In the master’s thesis, we aimed to identify proteins
that interact with human MATR3 and its mutant form MATR3S85C in vivo with the BioID 
method, which is based on labelling the nearby proteins with biotin. To this end, we 
generated cell lines stably expressing fusion protein of MATR3 or MATR3S85C with the 
biotin ligase BioID2 or BioID2 without a fusion partner. We found that fusion proteins
of MATR3 and MATR3S85C with the biotin ligase BioID2 have the same cellular 
localization as endogenous MATR3 and that BioID2 is enzymatically active. After 
examining the BioID2 activity and cellular localization of the expressed proteins, we 
successfully isolated biotinylated interaction partners of MATR3 and MATR3S85C from 
cell lysates by the pull-down assay. Using silver staining and immunodetection of the 
biotinylated proteins after Western blotting, we detected proteins specific for samples 
with MATR3 and MATR3S85C, but not for samples with BioID2 without a fusion partner. 
These interaction partners will be identified by liquid chromatography – mass 
spectrometry. Our results will help to understand MATR3 and MATR3S85C interactome.
Moreover, we have already detected two known MATR3 interaction partners, TDP-43 
and NONO in eluates with MATR3 and MATR3S85C. Finally, we have examined the 
effect of MATR3S85C on stress granule formation, and based on the results, we have
concluded that this form of MATR3 prevents their formation. | 
        
        
        
            | Secondary keywords: |  
            MATR3;ALS;interaction partners;BioID; | 
        
        
            
        
            | Type (COBISS): |  
            Master's thesis/paper | 
        
        
        
            | Study programme: |  
            1000377 | 
        
        
           
        
           
        
           
        
            | Embargo end date (OpenAIRE): |  
            2022-10-01 | 
        
        
           
        
            | Thesis comment: |  
            Univ. v Ljubljani, Fak. za kemijo in kemijsko tehnologijo, smer Biokemija | 
        
        
           
        
           
        
           
        
            | Pages: |  
            67 str. | 
        
        
           
        
           
        
           
        
           
        
           
        
           
        
           
        
           
        
          
        
          
        
          
        
         
        
         
        
        
            | ID: |  
            14047829 |